A Rare And Severe Complication Of SLE: Bullous Systemic Lupus Erythematous


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Authors

  • Rosdara Masayuni Mohd Sani Emergency Medicine Department, Monash University Malaysia, Clinical School Johor Bahru, 80100 Johor Bahru, Johor, Malaysia.
  • Chuan Yi Foo School of medicine, International Medical University, Clinical Campus, Jalan Rasah, 70300 Seremban, Negeri Sembilan, Malaysia.
  • Muhammad Mujibuddin Hassan School of medicine, International Medical University, Clinical Campus, Jalan Rasah, 70300 Seremban, Negeri Sembilan, Malaysia.
  • Michael Yang Song Lim School of medicine, International Medical University, Clinical Campus, Jalan Rasah, 70300 Seremban, Negeri Sembilan, Malaysia.
  • Chen Liang Tan School of medicine, International Medical University, Clinical Campus, Jalan Rasah, 70300 Seremban, Negeri Sembilan, Malaysia.
  • Ling Chian Voon School of medicine, International Medical University, Clinical Campus, Jalan Rasah, 70300 Seremban, Negeri Sembilan, Malaysia.

DOI:

https://doi.org/10.33102/mjosht.v8i.289

Keywords:

BSLE, Septic Shock, Therapeutics, Outcome

Abstract

Bullous systemic lupus erythematosus (BSLE) is a rare antibody-mediated blistering eruption of subepidermal tissues in patients with underlying SLE. We report a case of a 19 years old Indian unconscious male who presented with acute generalized blistering lesion and widespread tense vesicles and Bullae at the superior trunk, proximal superior limbs, and face(lips) with the symmetrical distribution. Bullae contained haemorrhagic fluid and bleeding was also seen on the ruptured site. The lesions are also seen on mucosal areas such as perioral, pharyngeal, laryngeal, and genital areas. Multiple erosions and crusting lesions are also seen over the body. Multiple scalp plaque erythematous peeling lesions with foul smells. Blood investigation showed leucocytosis and metabolic acidosis with a diagnosis of septic shock secondary to infected BSLE. He was treated with IV hydrocortisone 200mg, analgesic, and IV Ceftriaxone. Unfortunately, he collapsed 24 hours later and passed away. This case report highlights the importance of early detection of BSLE as an acute skin complication in patients with underlying SLE and its management steps.

 

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References

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Published

2022-09-21
CITATION
DOI: 10.33102/mjosht.v8i.289
Published: 2022-09-21

How to Cite

Rosdara Masayuni Mohd Sani, Chuan Yi Foo, Muhammad Mujibuddin Hassan, Michael Yang Song Lim, Chen Liang Tan, & Ling Chian Voon. (2022). A Rare And Severe Complication Of SLE: Bullous Systemic Lupus Erythematous. Malaysian Journal of Science Health & Technology, 8, 1–3. https://doi.org/10.33102/mjosht.v8i.289

Issue

Vol. 8 (2022): Special Issue on Communicable and Non-Communicable Disease, Multidisciplinary Case Reports

Section

Medical

Copyright (c) 2022 Rosdara Masayuni Mohd Sani, Chuan Yi Foo, Muhammad Mujibuddin Hassan, Michael Yang Song Lim, Chen Liang Tan, Ling Chian Voon

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